DYKE-DAVIDOFF-MASSON SYNDROME: A RARE CASE REPORT

Dr. Shyam Bihari Meena, Dr. Mayank Kumar Sharma, Dr. Shyoji Ram Meena

Abstract


Dyke–Davidoff–Masson syndrome (DDMS) is a rare condition, in which patient has cerebral hemiatrophy, seizures and mental retardation after some insult to the developing brain during fetal or infantile period. Diagnosis is mainly dependent upon clinical and radiological findings.  Here we are presenting a case of a 14 year old girl who came to us in altered sensorium after an episode of status epilepticus with left hemiparesis and cognitive impairment since childhood. CT of brain revealed right cerebral atrophy and hyperpneumatization of right frontal and mastoid sinuses characteristic of Dyke-Davidoff-Masson syndrome[DDMS].


Keywords


Cerebral hemiatrophy, Dyke–Davidoff–Masson syndrome, hemiparesis

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References


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