Nakul Pahwa, Suniti Kumar Saha


 Background:  Embryonal tumors  comprise a group of aggressive, poorly differentiated tumors occurring in central nervous system. Primary cerebellopontine angle (CPA) embryonal tumor is an extremely rare entity. It is important to have knowledge of this pathology and to be able to differentiate it from other commonly occurring CPA tumors, such as vestibular and trigeminal schwannomas. This distinction is essential because of the difference in the overall treatment plan and prognosis.

Case Description: This report describes a case of 4 year old girl who presented with headache and vomiting to our department. MRI findings suggested medulloblastoma and patient underwent surgery. Histopathology confirmed our diagnosis.

Conclusion: We discuss the importance of detecting this rare entity and distinguishing it from commonly occurring tumors in the CP angle region.


Cerebellopontine angle, embryonal, medulloblastoma, tumor, rare

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Louis DN, Ohgaki H, Wiestler OD, Cavenee WK, Burger PC, Jouvet A, et al. The 2007 WHO classification of tumours of the central nervous system. Acta Neuropathol 2007;114:97-109

Brackmann DE, Bartels LJ. Rare tumors of the cerebellopontine angle.Otolaryngol Head Neck Surg (1979) 1980;88:555-9

Kalamarides M, Dewolf E, Couvelard A, Shahidi A, Bouccara D,Cyna-Gorse F, et al. Extraaxial primitive neuroectodermal tumor mimicking a vestibular schwannoma: Diagnostic and therapeutic difficulties. Report of two cases. J Neurosurg 2001;94:612-6

Moffat DA, Saunders JE, McElveen JT Jr, McFerran DJ, Hardy DG. Unusual cerebello-pontine angle tumours. J Laryngol Otol 1993;107:1087-98.

5. Adesina AM, Tihan T, Fuller CE, et al., eds. Atlas of pediatric brain tumors. New York: Springer;2009.

6. Gaffney CC, Sloane JP, Bradley NJ, Bloom HJ. Primitive neuroectodermal tumours of the cerebrum. Pathology and treatment. J Neurooncol 1985;3:23-33.

7. Spina A, Boari N, Gagliardi F, Franzin A, Terreni MR, Mortini P. Review of cerebellopontine angle medulloblastoma. Br J Neurosurg 2013;27:316-20


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