ORBITAL CAVERNOUS HEMANGIOMA WITH LYMPHOVENOUS MALFORMATION

Dr. Sumaira Siddiqui, Dr. Deepti Gupta, Dr. Shefali Agarwal, Dr. Nupur Trivedi, Dr Anjali Tewari, Dr. Asha Agarwal

Abstract


Introduction: Cavernous hemangioma although not a true neoplasm, is the most common benign adult orbital tumour. The patient usually presents with painless slowly progressive bulging of the globe. An orbital venous-lymphatic malformation is a rare lesion. And a coexistence of orbital cavernous hemangioma with lymphovascular malformation is even more unusual with only a few case reports in the literature so far. Case Report: We hereby describe the clinical, radiological and histopathological features of a case of orbital cavernous hemangioma with coexisting lymphovenous malformation in an 11 year old girl child. The girl came to our ophthalmology department with a slowly increasing swelling on the medial aspect of her right eye ball since birth, which on histopathological examination revealed both cavernous haemangioma and lymphovenous malformation in coexistence. Conclusion: This entity represents an association of different types of orbital malformations with probably same pathogenesis.


Keywords


Cavernous haemangioma, lymphovenous malformation, coexistence, orbital

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References


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