PRIMARY AMELANOTIC MELANOMA OF THE RECTUM- A RARE CASE PRESENTATION.

S. P. Gayathre, R. Niranjan Kumar, R. Kannan, R. Jayachander

Abstract


Melanomas are primarily a disease of the skin as melanocytes are present abundantly in the skin. Melanocytes are also present in the eyes, nasal

Cavity, oropharynx, vagina, urinary tract, rectum, and anus. Though  rare , malignancies from melanocytes can arise from any of these areas.  Mucosal melanomas account for approximately 1.2% of all melanomas, and anorectal melanomas account for fewer than 25% of all mucosal melanomas. Amelanotic  melanoma of the anorectum is a very rare entity. Only  few cases have been identified and documented. Because of very low documented cases, treatment strategies have not been developed, which makes managing these cases a tough task. This is a 60 year male with no co morbidities, presenting with difficulty in defecation, later diagnosed to have primary ano - rectal  amelanotic melanoma.


Keywords


Melanomas, disease, treatment

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