ANAESTHESIA MANAGEMENT OF FEMUR FRACTURE FIXATION IN A PATIENT WITH FANCONI SYNDROME – A CASE REPORT

Dr. Harini. A, Dr. Anand Ram. A, Dr. Mrunalini. P

Abstract


Detoni Debre Fanconi syndrome also called as Renal Fanconi syndrome is a rare acquired or inherited condition involving generalised transport defect in the proximal convoluted tubule of nephron leading to renal loss of electrolytes or substances that are usually absorbed. The incidence rate of this syndrome is 1:40,000 live births. Here we present the anaesthesia management in a patient with Fanconi syndrome posted for fixation of fracture femur.


Keywords


Fanconi syndrome, Renal tubular acidosis

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References


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