POLAND SYNDROME,CONGENITAL DEFECT OF THE CHEST WALL:A CASE REPORT

Dr. Sagar S. Rashinkar, Dr. Prakash G. Mantur

Abstract


POLAND SYNDROME is rare disorder characterised by underdeveloped/ absent  chest muscle on one side of body. Incidence,l in 10,000 to 1 in 1,00,000.The authors describe a case of 65years old man,with history of breathlessness,on clinical examination of head to toe revealed defect of chest wall on left side.The authors presents a variant of poland's syndrome to empasize the risk of trauma to underlying cardia,may impair significant movement on one side of body, as condition is asymptomatic and often not diagnosed & psychological toll if diagnosed in teenagers .This is few of documented cases of poland's syndrome from india.


Keywords


poland syndrome,chest wall,sporadic.

Full Text:

PDF

References


. Ravitch MM. Poland’s syndrome. In: Ravitch MM, ed. Congenital deformities of the chest wall and their operative correction. Philadelphia, London, Toronto: WB Saunders, 1977:233–71.

. Urschel HC Jr, Byrd HS, Sethi SM, Razzuk MA. Poland’s syndrome: improved surgical management. Ann Thorac Surg 1984;37:204–11.

. Urschel HC. Poland’s syndrome. Chest Surg Clin N Am 2000;10:393–403.

. David TJ. The Poland anomaly and allied disorders. Pediatr Res 1981;15:1184.

. Shamberger RC, Welch KJ, Upton J III. Surgical treatment of thoracic deformity in Poland’s syndrome. J Pediatr Surg 1989;24:760–5.

. Karnak I, Tanyel FC, Tuncbilek E, U¨ nsal M, Bu¨ yu¨ kpamukcu N. Brief clinical report. Bilateral Poland anomaly. Am J Med Genet 1998;75:505–7.

. rarediseases.info.nih.gov/diseases/7412/poland-syndrome.

. Bavinck JNB, Weaver DD. Subclavian artery supply disruption sequence: hypothesis of a vascular etiology for Poland, Klippel-Feil, and Mo¨bius anomalies. Am J Med Genet 1986; 23:903–18.

. Hegde HR, Shokeir MH. Posterior shoulder girdle abnormalities with absence of pectoralis major muscle. Am J Med Genet 1982;13:285–93

. Hedge HR, Leung AKC. Aplasia of pectoralis major muscle and renal anomalies. Am J Med Genet 1989;32:109–11.

. Pranava VM, Rao PSSS, Neelachalam A, Sailendra VH. Poland’s syndrome with renal hypertension. JAPI 2000;48: 452–3.

. Alexander A. Fokin, MD, PhD, and Francis Robicsek, MD, PhD. Poland’s Syndrome Revisited. Ann Thorac Surg 2002;74:2218–25).


Refbacks

  • There are currently no refbacks.