A CASE OF PROBABLE SJOGRENS SYNDROME PRESENTING WITH HYPOKALEMIC PARALYSIS AND INCIDENTAL CHRONIC HEPATITIS B VIRUS INFECTION

Dr. Krishna Sagar Gajula, Dr. Vijay Karthik Bhogaraju, Dr. B. Sailaja, DR. Y. V. L. Narasimham

Abstract


Sjogren’s syndrome is relatively rare in males, with female to male incidence ratio of 16:1. It is an autoimmune disorder characterized by lymphocytic infiltration of exocrine glands. However, the disease may be associated with extra glandular manifestation affecting multiple organs.

We report one such uncommon presentation where a 19-year-old male was brought to our emergency department with chief complaint of weakness of all four limbs. He had hypokalemia at admission.

Upon further evaluation, we diagnosed this case as probable Sjogren’s syndrome with distal renal tubular acidosis (dRTA) which caused the hypokalemia.

Incidentally he was found having chronic hepatitis B virus infection. This association of hepatitis virus infection and Sjogren’s syndrome is rarely described in the literature.

Keywords


Sjogren’s Syndrome, distal Renal Tubular Acidosis, hypokalemic paralysis, Hepatitis B.

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References


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