VANISHING BONES – GORHAM IDIOPATHIC OSTEOLYSIS. A RARE DISEASE.

Sultan Nawahirsha, David Mathew, Tahiri putta, Ramya I

Abstract


Gorham’s disease is a rare osteolytic disease of unknown etiology. It is characterized by massive osteolytic resorption of the bone which is replaced by lymphangiomatosis of the bone(1). It is also known as Gorham Stout disease, disappearing bone disease and idiopathic osteolysis.(2)The diagnosis is established with bone biopsy and evidence of progressive osseous resorption in imaging (3). Here, we report a case of a 27 year old male who presented with chronic holo-cranial headache and bilateral sensorineuronal hearing loss. On investigations, he was found to have multiple well circumscribed lytic lesions and his biopsy revealed benign angiomatous lesion thus fulfilling the diagnostic criteria proposed by heffez and colleagues in 1983. He was managed with bisphosphonates. 


Keywords


VANISHING BONES, osteolytic disease, lymphangiomatosis

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References


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