Dr. Pradhyumna Koushik T. P., Prof. Dr. Mohanapriya T., Prof. Dr. K. Balaji Singh, Dr. Manuneethi Maran, Dr. Nitesh


One of the rarest variety of disorders of sexual differentiation (DSD) is true hermaphrodite and it represents only 5% of all cases.  These cases usually present in early childhood or late adolescence with ambiguous genitalia. We are here reporting a rare case of a true hermaphrodite at 30 years of age with two cellular lines (46XX/46XY), small testis, hypospadias and breast pain. Histology of the gonads revealed right ovotestes.



True hermaphrodite, ovo-testes, sexual differentiation disorders

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